Marfan Syndrome Patients Life Expectancy

Both children and adults can live marfan syndrome as long as they engage in appropriate medical care, receive accurate information from their doctor and social support to make living with the disease more manageable. Among the patients, 166 (76.2) were college graduates, 150 (69.2) were employed, and 145 (66.5 %) were married.

Life Expectancy And Causes Of Death In The Marfan Syndrome Nejm

“marfan syndrome patients now almost have normal life expectancy because of advances in recognition of the disease, treatment and better outcomes with surgery,” vidyasagar kalahasti, md.

Marfan syndrome patients life expectancy. The average age at death for the 72 deceased patients was 32. The life expectancy in this syndrome has increased to greater than 25% since 1972. April 23 i am 18 years old and i am new to the knowledge of marfan syndrome.

This poor survival was demonstrated in a series of 257 patients with the marfan syndrome. Having marfan syndrome does not mean patients might not acquire other conditions that are common in the aging population. In conclusion, life expectancy for patients with the marfan syndrome has increased >25% since 1972.

Patients undergoing surgery after 1980 enjoyed significantly increased survival than patients who had undergone operation before 1980 (p = 0.008). However, there are no guarantees. People who are accurately diagnosed, adapt proper lifestyles and receive appropriate medical and surgical management may live for a normal life span (into their 70s).

At the moment, reports state that life expectancy for patients with marfan syndrome is around seventy years of age. In total, 137 (62.8 %) of the patients were men and the mean age was 36.3 ± 4.5 years. So to all parent's and families of marfans patients, hang in there and cherish every day with your loved one and stay strong.

In conclusion, life expectancy for patients with the marfan syndrome has increased >25% since 1972. Few patients with marfan syndrome live out a normal life span. It generally makes you very long and lanky, but this condition comes with a lot more dangerous things.

Silverman et al., 1995 ) primarily due to increased risk of aortic pathology,. Despite the high risk for marfan related cardiovascular problems, the average life expectancy of those with marfan syndrome is nearly 70 years. Nowadays, people with marfan syndrome live until age 70, which is comparable to the average life expectancy of the general population.

Several reports indicate that lifespan is shortened (murdoch, walker, halpern, kuzma, & mckusick, 1972 ; The average lifespan is now approximately 70. However, this is a really exciting time for patients with the condition as we now have new drugs which we can use to give to even very young children who are affected to reduce or maybe even stop aortic root enlargement.

Marfan syndrome is a rare connective tissue disorder, which affects your bones and joints, and things such as that. In our experience, patients who underwent isolated supracoronary ascending aorta or root replacement showed the most satisfactory late survival. Over the past 30 years, we have witnessed a steady improvement in life expectancy of patients with marfan syndrome, owing to advances in various treatments.

The mean height of the patients was 178.4 ± 12.5 cm. Wang r, ma wg, tian lx, sun lz, chang q. The mean life expectancy for untreated patients with marfan syndrome is 32 years with aortic dissection, aortic rupture or cardiac failure due to mitral and aortic valve regurgitation as the predominant cause of death in > 90% of the cases.

Before the evolution of open heart surgery, however, marfan patients usually died from acute aortic dissection or rupture, and thus had an average life‐expectancy of only 32 years.

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